kodex

Kodex

ICD-10-CM
Section

D81.81

Biotin-dependent carboxylase deficiency

Hierarchy

  • D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
    • D80-D89 Certain disorders involving the immune mechanism (D80-D89)
      • D81 Combined immunodeficiencies
        • D81.8 Other combined immunodeficiencies
          • D81.81 Biotin-dependent carboxylase deficiency
            • D81.810 Biotinidase deficiency
            • D81.818 Other biotin-dependent carboxylase deficiency
            • D81.819 Biotin-dependent carboxylase deficiency, unspecified

Inclusion Terms

D81.81

  • Multiple carboxylase deficiency

Includes

D80-D89

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes 1

D81.81

  • biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
    • E53.8 Deficiency of other specified B group vitamins

D81

  • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
    • D80.0 Hereditary hypogammaglobulinemia

D80-D89

  • autoimmune disease (systemic) NOS (M35.9)
    • M35.9 Systemic involvement of connective tissue, unspecified
  • D71 Functional disorders of polymorphonuclear neutrophils
  • B20 Human immunodeficiency virus [HIV] disease

Excludes 2

D50-D89

  • autoimmune disease (systemic) NOS (M35.9)
    • M35.9 Systemic involvement of connective tissue, unspecified
  • P00-P96 Certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • O00-O9A Pregnancy, childbirth and the puerperium (O00-O9A)
  • Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • B20 Human immunodeficiency virus [HIV] disease
  • S00-T88 Injury, poisoning and certain other consequences of external causes (S00-T88)
  • C00-D49 Neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)