kodex

Kodex

ICD-10-CM
Code

E71.541

Zellweger-like syndrome

Copy Code Send Code

Hierarchy

  • E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
    • E70-E88 Metabolic disorders (E70-E88)
      • E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
        • E71.5 Peroxisomal disorders
          • E71.54 Other peroxisomal disorders
            • E71.540 Rhizomelic chondrodysplasia punctata
            • E71.541 Zellweger-like syndrome
            • E71.542 Other group 3 peroxisomal disorders
            • E71.548 Other peroxisomal disorders

Notes

E00-E89

  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    • E07.0 Hypersecretion of calcitonin
    • E34 Other endocrine disorders

Excludes 1

E71.5

  • Schilder's disease (G37.0)
    • G37.0 Diffuse sclerosis of central nervous system

E70-E88

  • E34.5 Androgen insensitivity syndrome
  • congenital adrenal hyperplasia (E25.0)
    • E25.0 Congenital adrenogenital disorders associated with enzyme deficiency
  • hemolytic anemias attributable to enzyme disorders (D55.-)
    • D55 Anemia due to enzyme disorders
  • Q87.4 Marfan syndrome
  • 5-alpha-reductase deficiency (E29.1)
    • E29.1 Testicular hypofunction

E00-E89

  • P70-P74 Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes 2

E70-E88

  • Q79.6 Ehlers-Danlos syndromes

Related Terms