Kodex

Code

Q56.1

Male pseudohermaphroditism, not elsewhere classified

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Hierarchy

Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- Q50-Q56 Congenital malformations of genital organs (Q50-Q56)
  - Q56 Indeterminate sex and pseudohermaphroditism
    - Q56.0 Hermaphroditism, not elsewhere classified
    - Q56.1 Male pseudohermaphroditism, not elsewhere classified
    - Q56.2 Female pseudohermaphroditism, not elsewhere classified
    - Q56.3 Pseudohermaphroditism, unspecified
    - Q56.4 Indeterminate sex, unspecified

Notes

Codes from this chapter are not for use on maternal records

Inclusion Terms

Q56.1

46, XY with streak gonads
Male pseudohermaphroditism NOS

Excludes 1

46,XX true hermaphrodite (Q99.1)
- Q99.1 46, XX true hermaphrodite
E34.5 Androgen insensitivity syndrome
chimera 46,XX/46,XY true hermaphrodite (Q99.0)
- Q99.0 Chimera 46, XX/46, XY
female pseudohermaphroditism with adrenocortical disorder (E25.-)
- E25 Adrenogenital disorders
pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
pure gonadal dysgenesis (Q99.1)
- Q99.1 46, XX true hermaphrodite

E34.5 Androgen insensitivity syndrome
syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)
- Q90-Q99 Chromosomal abnormalities, not elsewhere classified (Q90-Q99)

Excludes 2

inborn errors of metabolism (E70-E88)
- E70-E88 Metabolic disorders (E70-E88)